Peripheral Primitive Neuroectodermal Tumor with Osseous Component of the Small Bowel Mesentery: A Case Study
- Authors
- Kim, Joon Mee; Chu, Young Chae; Choi, Chang Hwan; Kim, Lucia; Choi, Suk Jin; Park, In Suh; Han, Jee Young; Kim, Kyung Rae; Choi, Yoon-La; Kim, Taeeun
- Issue Date
- Feb-2013
- Publisher
- KOREAN SOCIETY PATHOLOGISTS
- Keywords
- Neuroectodermal tumor; primitive; peripheral; Intestine, small; Osteogenesis; Metaplasia; EWSR1
- Citation
- KOREAN JOURNAL OF PATHOLOGY, v.47, no.1, pp.77 - 81
- Journal Title
- KOREAN JOURNAL OF PATHOLOGY
- Volume
- 47
- Number
- 1
- Start Page
- 77
- End Page
- 81
- URI
- https://scholarworks.bwise.kr/gachon/handle/2020.sw.gachon/14801
- DOI
- 10.4132/KoreanJPathol.2013.47.1.77
- ISSN
- 1738-1843
- Abstract
- A case of peripheral primitive neuroectodermal tumor of the small bowel mesentery with osseous component is reported. A 23-year-old man was admitted to our hospital because of acute severe abdominal pain. Abdominal computed tomography revealed a large solid and cystic, oval shaped mass, measuring 11.0 x 6.0 cm in the pelvic cavity. Histologically the resected lesion consisted of sheets of undifferentiated small round cells forming Homer-Wright rosettes and perivascular pseudorosettes, and showed areas of osteoid and bone formation. lmmunohistochemical studies revealed that tumor cells expressed positivity against CD99 (MIC2), CD57, neuron-specific enolase, and vimentin. Fluorescence in situ hybridization study revealed Ewing sarcoma breakpoint region 1 (EWSR1) gene rearrangement on chromosome 22q12. To the authors' knowledge this is the first documentation of a peripheral neuroectodermal tumor with osteoid and bone formation of the small bowel mesentery.
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