A Case of Wilms Tumor with a Tumor Thrombus in a Boy with WAGR SyndromeA Case of Wilms Tumor with a Tumor Thrombus in a Boy with WAGR Syndrome
- Other Titles
- A Case of Wilms Tumor with a Tumor Thrombus in a Boy with WAGR Syndrome
- Authors
- Soojung Lee; Hyo Jin Kim; In-sang Jeon
- Issue Date
- Oct-2020
- Publisher
- 대한소아혈액종양학회
- Keywords
- .; WAGR syndrome; Wilms tumor; Tumor thrombus; Inferior vena cava
- Citation
- Clinical Pediatric Hematology-Oncology, v.27, no.2, pp.134 - 137
- Journal Title
- Clinical Pediatric Hematology-Oncology
- Volume
- 27
- Number
- 2
- Start Page
- 134
- End Page
- 137
- URI
- https://scholarworks.bwise.kr/gachon/handle/2020.sw.gachon/78782
- DOI
- 10.15264/cpho.2020.27.2.134
- ISSN
- 2233-5250
- Abstract
- Intravascular extension of Wilms tumor (WT) can occur in approximately 4-10% of patients. In general, it does not cause any clinical problems because most of these tumors are small. Although there is no standard treatment currently, preoperative chemotherapy and delayed nephrectomy is generally recommended for children with WT accompanied by tumor thrombus. We report a rare case of WT, aniridia, genitourinary anomalies, and mental retardation (WAGR) syndrome in a boy who also had a huge inferior vena cava thrombus, 7 cm length. The prevalence of bilateral WT and tumor thrombus in WAGR has not been identified. The patient was successfully treated with neoadjuvant chemotherapy to decrease the size of the tumor thrombus with WT and delayed nephrectomy following chemotherapy without any invasive intervention and did not show complications.
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Collections - 의과대학 > 의학과 > 1. Journal Articles
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