Pulmonary arterial hypertension due to antiphospholipid syndrome initially mimicking chronic thromboembolic pulmonary hypertension
- Authors
- Yeo, Jina; Shin, Nami; Ahn, Kyung-Jin; Seo, Miryoung; Jang, Albert Youngwoo; Kim, Minsu; Chung, Wook-Jin
- Issue Date
- Apr-2022
- Publisher
- SPRINGERNATURE
- Keywords
- Pulmonary arterial hypertension; Antiphospholipid syndrome; Thromboembolism; Endothelin receptor antagonist
- Citation
- CLINICAL HYPERTENSION, v.28, no.1, pp.10 - 13
- Journal Title
- CLINICAL HYPERTENSION
- Volume
- 28
- Number
- 1
- Start Page
- 10
- End Page
- 13
- URI
- https://scholarworks.bwise.kr/gachon/handle/2020.sw.gachon/84040
- DOI
- 10.1186/s40885-021-00191-1
- ISSN
- 2635-6325
- Abstract
- Pulmonary arterial hypertension (PAH) is the second most common lung complication in antiphospholipid syndrome (APS) patients. However, the concurrent development of APS-related nonthrombotic PAH is rarely reported. Lack of awareness for group 1 PAH in APS patient may contribute to underdiagnosis of this condition. Herein, we reviewed the case of a 56-year-old female who was diagnosed with PAH related to APS that mimicked chronic thromboembolic pulmonary hypertension (CTEPH). It is crucial to be aware of the possibility of a group 1 PAH diagnosis, even though patients have already been diagnosed with CTEPH. Furthermore, a multidisciplinary approach and serial follow-up right heart catheterization with echocardiography are important to make a timely diagnosis and provide optimal treatment for APS-related PAH in patients with CTEPH-like clinical features.
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Collections - 의과대학 > 의학과 > 1. Journal Articles
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