Extrapulmonary lymphangioleiomyoma presenting as a mesenteric cystic mass
- Authors
- Jun, Young Jin; Jang, Se Min; Han, Hulin; Jang, Ki-Seok; Paik, Seung Sam
- Issue Date
- Jun-2011
- Publisher
- Wiley-Blackwell
- Keywords
- Extrapulmonary; Lymphangiomyoma; Mesentery
- Citation
- Basic and Applied Pathology, v.4, no.2, pp.63 - 65
- Indexed
- SCOPUS
- Journal Title
- Basic and Applied Pathology
- Volume
- 4
- Number
- 2
- Start Page
- 63
- End Page
- 65
- URI
- https://scholarworks.bwise.kr/hanyang/handle/2021.sw.hanyang/168255
- DOI
- 10.1111/j.1755-9294.2011.01097.x
- ISSN
- 1755-9294
- Abstract
- Lymphangioleiomyoma (LAM) is a rare benign tumor characterized by a disorganized smooth muscle cell proliferation within the walls of pulmonary, mediastinal, and retroperitoneal lymphatic vessels. The mesenteric LAM is a quite unusual presentation. A 47-year-old woman was admitted to our hospital with a 7-year history of abdominal mass. A computed tomography showed a well marginated mass with soft tissue attenuation. Laparoscopic excision was performed. The specimen revealed a well circumscribed dark cystic mass. The cut surface showed a thin walled cystic tumor with haphazardly distributed trabeculated septa. Microscopically, the tumor showed variable sized ectatic spaces lined by flattened endothelial cells and surrounded by epithelioid or spindle-shaped cells. The lining cells were positive for D2-40, CD31, and CD34. The surrounding cells were positive for alpha-smooth muscle actin and human melanoma black-45. The final diagnosis was a solitary LAM arising in the mesentery. The patient showed an uneventful postoperative course for 10 months.
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