단세포군 감마글로불린병증을 동반한 경화점액수종Scleromyxedema with Monoclonal Gammopathy
- Authors
- 심현철; 김건; 최지현; 김지혜; 김은정; 박향준; 조옥자; 송계용
- Issue Date
- May-2011
- Publisher
- 대한피부과학회
- Keywords
- Lichen myxedematosus; Monoclonal gammopathy; Scleromyxedema
- Citation
- 대한피부과학회지, v.49, no.05, pp 440 - 443
- Pages
- 4
- Journal Title
- 대한피부과학회지
- Volume
- 49
- Number
- 05
- Start Page
- 440
- End Page
- 443
- URI
- https://scholarworks.bwise.kr/cau/handle/2019.sw.cau/33235
- ISSN
- 0494-4739
- Abstract
- Scleromyxedema is a rare disorder characterized by generalized papular and sclerodermoid eruption, increased fibroblast proliferation, mucin deposition, and monoclonal gammopathy in the absence of thyroid disease. It is a generalized subtype of lichen myxedematosus. A paraproteinemia, typically an IgG λ, is observed in more than 80% of patients with scleromyxedema. Here, we report a 38-year-old woman with a 1-year history of a progressively spreading of eruption of small papules on the entire body, including the face, neck, arms, legs, and trunk. Laboratory tests were within normal limits, except λ light chain monoclonal gammopathy. We administered oral retinoid and topical steroid with slight clinical improvement. To our knowledge, this is the first reported case of scleromyxedema in Korea. (Korean J Dermatol 2011;49(5):440∼443)
- Files in This Item
- There are no files associated with this item.
- Appears in
Collections - Law School > Law > 1. Journal Articles
Items in ScholarWorks are protected by copyright, with all rights reserved, unless otherwise indicated.